Nevoid Basal Cell Carcinoma Syndrome : A Case Report (기저세포모반증후군 : 증례 보고)

이윤정; 박재홍; Chul Choi Sung (최성철); 이수언; KIM， KWANG CHUL (김광철)

doi:10.5933/JKAPD.2014.41.1.34

Nevoid Basal Cell Carcinoma Syndrome : A Case Report

Journal of the Korean academy of pediatric dentistry
Abbr : J Korean Acad Pediatr Dent
2014, 41(1), pp.34-39
DOI : 10.5933/JKAPD.2014.41.1.34
Publisher : The Korean Academy Of Pediatric Dentistry
Research Area : Medicine and Pharmacy > Dentistry

이윤정 ¹, 박재홍 ², Chul Choi Sung ², 이수언 ³, KIM， KWANG CHUL ²

¹강동경희대학교병원 치과병원 소아치과
²경희대학교
³경희대학교 치의학전문대학원 소아치과학교실

Accredited

ABSTRACT

Nevoid basal cell carcinoma syndrome(NBCCS) is a autosomal dominant disorder, and its major manifestationsare multiple basal cell carcinoma, keratocystic odontogenic tumor, rib anomalies, palmer and plantar pits,calcification of the falx cerebri. Keratocystic odontogenic tumor(KCOT) is defined as intraosseous tumor ofodontogenic origin with a characteristic lining of parakeratinized stratified squamous epithelium and potentialaggressive behavior. We report a case of a 3-year-old patient with nevoid basal cell carcinoma syndrome whoinitially presented with unilocular keratocystic odontogenic tumor in maxillary canine region. Keratocysticodontogenic tumor was treated by enucleation, and periodic follow-up check will be required for early diagnosisof additional diseases related with this syndrome.

KEYWORDS

Nevoid basal cell carcinoma syndrome, Keratocystic odontogenic tumor, Enucleation

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Journal of the Korean academy of pediatric dentistry 2023 KCI Impact Factor : 0.48

Nevoid Basal Cell Carcinoma Syndrome : A Case Report

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* References for papers published after 2023 are currently being built.

Journal of the Korean academy of pediatric dentistry 2023 KCI Impact Factor : 0.48

Nevoid Basal Cell Carcinoma Syndrome : A Case Report

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