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Familial Occurrence of Dentin Dysplasia Type I: Case Report

  • Journal of the Korean academy of pediatric dentistry
  • Abbr : J Korean Acad Pediatr Dent
  • 2014, 41(1), pp.47-53
  • DOI : 10.5933/JKAPD.2014.41.1.47
  • Publisher : The Korean Academy Of Pediatric Dentistry
  • Research Area : Medicine and Pharmacy > Dentistry

김소현 1 김영진 2 Kim, Hyun - Jung 2 NAM Soon-Hyeun 2

1경북대학교 치의학전문대학원 소아치과학교실
2경북대학교

Accredited

ABSTRACT

Dentin dysplasia is a rare hereditary disturbance characterized by a dental anomaly of the dentin layer. Theetiology is unclear, and this rare hereditary disturbance affects approximately one person in every 100,000. Dentin dysplasia is classified into two types, radicular dentin dysplasia as type I and coronal dentin dysplasia astype II. The characteristic clinical findings of dentin dysplasia type I are normal appearance of the crown andhypermobility of teeth. The radiographic findings are obliteration of all pulp canals, short, blunted and malformedor absent roots. Dentin dysplasia type II as coronal dentin dysplasia shows similar clinical features withdentinogensis imperfecta. This report shows a case of dentin dysplasia type I affecting one family except the father. The clinical, radiographicand histopathologic findings of this family are presented. Dentin dysplasia type I is difficult to diagnose unless dentist performs radiographic examination. If the affectingpatient does not get regular dental care, dental abscesses or cysts may form spontaneously without caries. Inthis regard, early diagnosis is important to prevent premature loss of dentition.

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