Basal Cell Nevus Syndrome : A Case Report (기저세포 모반 증후군 : 증례보고)

김지연; Sohee Oh (오소희)

doi:10.5933/JKAPD.2014.41.2.166

Basal Cell Nevus Syndrome : A Case Report

Journal of the Korean academy of pediatric dentistry
Abbr : J Korean Acad Pediatr Dent
2014, 41(2), pp.166~173
DOI : 10.5933/JKAPD.2014.41.2.166
Publisher : The Korean Academy Of Pediatric Dentistry
Research Area : Medicine and Pharmacy > Dentistry

김지연 ¹, Sohee Oh ²

¹한림대학교 성심병원 소아치과
²한림대학교

Accredited

ABSTRACT

The basal cell nevus syndrome is also known as the Gorlin-Goltz syndrom. It is a dominant autosomal disorderwhich is characterized by keratocystic odontogenic tumors in the jaw, skeletal abnormalities, and multiple basalcell nevi carcinomas. This study reports an 11-year-old boy with multiple odontogenic keratocysts in the jaw,hypertelorism, and frontal bossing. When a young patient has cystic lesions with an impacted permanent teeth,it is important to preserve the teeth. For a growing patient with impacted permanent teeth, a more conservativemethod is suggested, which will enable the preservation the permanent teeth in Gorlin-Goltz syndrome.

KEYWORDS

Basal cell nevus syndrome, Impacted permanent teeth, Keratocystic odontogenic tumor

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Journal of the Korean academy of pediatric dentistry 2025 KCI Impact Factor : 0.43

Basal Cell Nevus Syndrome : A Case Report

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Journal Copyright Policy

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* References for papers published after 2025 are currently being built.

Journal of the Korean academy of pediatric dentistry 2025 KCI Impact Factor : 0.43

Basal Cell Nevus Syndrome : A Case Report

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KEYWORDS

Journal Copyright Policy

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