@article{ART001994826},
author={최시내 and 김영진 and NAM Soon-Hyeun and Kim, Hyun - Jung},
title={Incontinentia Pigmenti with Multiple Missing Teeth : Case Reports},
journal={Journal of the Korean academy of pediatric dentistry},
issn={1226-8496},
year={2015},
volume={42},
number={2},
pages={180-187},
doi={10.5933/JKAPD.2015.42.2.180}
TY - JOUR
AU - 최시내
AU - 김영진
AU - NAM Soon-Hyeun
AU - Kim, Hyun - Jung
TI - Incontinentia Pigmenti with Multiple Missing Teeth : Case Reports
JO - Journal of the Korean academy of pediatric dentistry
PY - 2015
VL - 42
IS - 2
PB - The Korean Academy Of Pediatric Dentistry
SP - 180
EP - 187
SN - 1226-8496
AB - Incontinentia pigmenti, also called Bloch-Sulzberger syndrome, is a rare X-linked inherited dominant disorder that affects females, but causes spontaneous abortion of prenatal males. Incontinentia pigmenti is a systemic disease with clinical features similar to ectodermal dysplasia, including congenitally missing teeth. The pathogenesis is related to gene mutations in NF-kappa-B essential modulator on chromosome Xq28.
Incontinentia pigmenti is caused by a defect in the developmental stage of organs originating from the ectoderm or mesoderm and involves the skin, eyes, hair, teeth and central nervous system. This report discusses the management of three cases of 3 to 5 years old females with incontinentia pigmenti and accompanying multiple missing teeth. The cases had sparse hair, and showed oligodontia and anomalous crowns with supplementary cusps in the posterior teeth and conical anterior teeth. Removable space maintainers were applied, achieving improved esthetics, recovery of mastication and increased self-esteem in the patients.
KW - Incontinentia pigmenti;Congenital missing;Ectodermal dysplasia
DO - 10.5933/JKAPD.2015.42.2.180
ER -
최시내, 김영진, NAM Soon-Hyeun and Kim, Hyun - Jung. (2015). Incontinentia Pigmenti with Multiple Missing Teeth : Case Reports. Journal of the Korean academy of pediatric dentistry, 42(2), 180-187.
최시내, 김영진, NAM Soon-Hyeun and Kim, Hyun - Jung. 2015, "Incontinentia Pigmenti with Multiple Missing Teeth : Case Reports", Journal of the Korean academy of pediatric dentistry, vol.42, no.2 pp.180-187. Available from: doi:10.5933/JKAPD.2015.42.2.180
최시내, 김영진, NAM Soon-Hyeun, Kim, Hyun - Jung "Incontinentia Pigmenti with Multiple Missing Teeth : Case Reports" Journal of the Korean academy of pediatric dentistry 42.2 pp.180-187 (2015) : 180.
최시내, 김영진, NAM Soon-Hyeun, Kim, Hyun - Jung. Incontinentia Pigmenti with Multiple Missing Teeth : Case Reports. 2015; 42(2), 180-187. Available from: doi:10.5933/JKAPD.2015.42.2.180
최시내, 김영진, NAM Soon-Hyeun and Kim, Hyun - Jung. "Incontinentia Pigmenti with Multiple Missing Teeth : Case Reports" Journal of the Korean academy of pediatric dentistry 42, no.2 (2015) : 180-187.doi: 10.5933/JKAPD.2015.42.2.180
최시내; 김영진; NAM Soon-Hyeun; Kim, Hyun - Jung. Incontinentia Pigmenti with Multiple Missing Teeth : Case Reports. Journal of the Korean academy of pediatric dentistry, 42(2), 180-187. doi: 10.5933/JKAPD.2015.42.2.180
최시내; 김영진; NAM Soon-Hyeun; Kim, Hyun - Jung. Incontinentia Pigmenti with Multiple Missing Teeth : Case Reports. Journal of the Korean academy of pediatric dentistry. 2015; 42(2) 180-187. doi: 10.5933/JKAPD.2015.42.2.180
최시내, 김영진, NAM Soon-Hyeun, Kim, Hyun - Jung. Incontinentia Pigmenti with Multiple Missing Teeth : Case Reports. 2015; 42(2), 180-187. Available from: doi:10.5933/JKAPD.2015.42.2.180
최시내, 김영진, NAM Soon-Hyeun and Kim, Hyun - Jung. "Incontinentia Pigmenti with Multiple Missing Teeth : Case Reports" Journal of the Korean academy of pediatric dentistry 42, no.2 (2015) : 180-187.doi: 10.5933/JKAPD.2015.42.2.180
