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Dental Management in a Patient with Infantile Osteopetrosis : A Case Report with a 7-Year follow-up

  • Journal of the Korean academy of pediatric dentistry
  • Abbr : J Korean Acad Pediatr Dent
  • 2018, 45(2), pp.257-264
  • DOI : 10.5933/JKAPD.2018.45.2.257
  • Publisher : The Korean Academy Of Pediatric Dentistry
  • Research Area : Medicine and Pharmacy > Dentistry
  • Received : October 11, 2017
  • Accepted : November 23, 2017
  • Published : May 31, 2018

Minkyoung Cheon 1 Sunmi Yang 2 Jaehwan Kim 3 Choi Nam-Ki 4 Kim Seon Mi 4

1전남대학교 치과대학 소아치과학교실
2전남대학교 치의학전문대학원 소아치과학교실
3전남대학교병원
4전남대학교

Accredited

ABSTRACT

Osteopetrosis is characterized by impaired osteoclast function and increased bone density. Infantile osteopetrosis is a severe form of the disease and has characteristics such as diffusely sclerotic skeleton, pancytopenia, cranial nerve entrapment, infection susceptibility, and abnormal craniofacial appearance. Patients with infantile osteopetrosis often experience developmental delay, and may have a short life span. A 14-month-old girl with osteopetrosis presented to the department of pediatric dentistry. Incipient caries on deciduous incisors were observed. The patient revisited 4 years of age. Besides medical problems, oral complications such as growth retardation, narrow upper arch, crowding, dental caries, and abnormal tooth development were observed. After consultation with her pediatrician, dental treatments were performed on the deciduous molars under sedation after a prophylactic antibiotic injection. At a periodic follow-up, multiple deciduous teeth were treated and extracted, and oralrehabilitation with a removable partial denture was initiated. Patient with osteopetrosis are highly susceptible to infection because of their compromised immune system and problems associated with wound healing that lead to osteomyelitis or sepsis development. Active participation in dental care for sugar intake management and proper oral hygiene are obligatory.

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