Dental Management in a Patient with Infantile Osteopetrosis : A Case Report with a 7-Year follow-up

Minkyoung Cheon (천민경); Sunmi Yang (양선미); Jaehwan Kim (김재환); Choi Nam-Ki (최남기); Kim Seon Mi (김선미)

doi:10.5933/JKAPD.2018.45.2.257

Dental Management in a Patient with Infantile Osteopetrosis : A Case Report with a 7-Year follow-up

Journal of the Korean academy of pediatric dentistry
Abbr : J Korean Acad Pediatr Dent
2018, 45(2), pp.257-264
DOI : 10.5933/JKAPD.2018.45.2.257
Publisher : The Korean Academy Of Pediatric Dentistry
Research Area : Medicine and Pharmacy > Dentistry
Received : October 11, 2017
Accepted : November 23, 2017
Published : May 31, 2018

Minkyoung Cheon ¹, Sunmi Yang ², Jaehwan Kim ³, Choi Nam-Ki ⁴, Kim Seon Mi ⁴

¹전남대학교 치과대학 소아치과학교실
²전남대학교 치의학전문대학원 소아치과학교실
³전남대학교병원
⁴전남대학교

Accredited

ABSTRACT

Osteopetrosis is characterized by impaired osteoclast function and increased bone density. Infantile osteopetrosis is a severe form of the disease and has characteristics such as diffusely sclerotic skeleton, pancytopenia, cranial nerve entrapment, infection susceptibility, and abnormal craniofacial appearance. Patients with infantile osteopetrosis often experience developmental delay, and may have a short life span. A 14-month-old girl with osteopetrosis presented to the department of pediatric dentistry. Incipient caries on deciduous incisors were observed. The patient revisited 4 years of age. Besides medical problems, oral complications such as growth retardation, narrow upper arch, crowding, dental caries, and abnormal tooth development were observed. After consultation with her pediatrician, dental treatments were performed on the deciduous molars under sedation after a prophylactic antibiotic injection. At a periodic follow-up, multiple deciduous teeth were treated and extracted, and oralrehabilitation with a removable partial denture was initiated. Patient with osteopetrosis are highly susceptible to infection because of their compromised immune system and problems associated with wound healing that lead to osteomyelitis or sepsis development. Active participation in dental care for sugar intake management and proper oral hygiene are obligatory.

KEYWORDS

Infantile osteopetrosis, Oral complication, Dental management, Oral rehabilitation

Citation status

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Journal of the Korean academy of pediatric dentistry 2023 KCI Impact Factor : 0.48

Dental Management in a Patient with Infantile Osteopetrosis : A Case Report with a 7-Year follow-up

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* References for papers published after 2023 are currently being built.

Journal of the Korean academy of pediatric dentistry 2023 KCI Impact Factor : 0.48

Dental Management in a Patient with Infantile Osteopetrosis : A Case Report with a 7-Year follow-up

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