Dental Management in a Patient with Turner Syndrome with Dental Anomalies : A Case Report

Haney Lee (이한이); Seyoung Shin (신세영); KIM JAE GON (김재곤); LEE DAE-WOO (이대우); Yang Yeon Mi (양연미)

doi:10.5933/JKAPD.2018.45.3.386

Dental Management in a Patient with Turner Syndrome with Dental Anomalies : A Case Report

Journal of the Korean academy of pediatric dentistry
Abbr : J Korean Acad Pediatr Dent
2018, 45(3), pp.386-392
DOI : 10.5933/JKAPD.2018.45.3.386
Publisher : The Korean Academy Of Pediatric Dentistry
Research Area : Medicine and Pharmacy > Dentistry
Received : March 25, 2018
Accepted : May 24, 2018
Published : August 31, 2018

Haney Lee ¹, Seyoung Shin ², KIM JAE GON ³, LEE DAE-WOO ³, Yang Yeon Mi ³

¹전북대학교 치의학전문대학원 소아치과학교실 및 구강생체과학연구소
²전북대학교 치의학 전문대학원 소아치과학교실 및 구강생체과학연구소
³전북대학교

Accredited

ABSTRACT

Turner syndrome (TS) is a chromosomal disorder caused by monosomy of the X chromosome, with complete or partial absence of the second sex chromosome. Anomalies of root morphology have been found to occur more often in patients with TS, which make endodontic treatment challenging and requires special handling. The patients with TS may also have systematic problems such as cardiac or renal malformations, so in treating these patients it is important for clinicians not only to be aware of the characteristic intraoral findings, but also to make the patients have regular dental check-ups to prevent oral complications in advance. An 12-year-old girl who had been diagnosed with TS at the age of 10 years was referred due to discomfort in the bilateral mandibular premolar regions. Dens evaginatus and taurodontism were detected in all the mandibular premolars characteristically. The bilateral mandibular first premolars had three roots and the bilateral mandibular second premolars had periapical lesion with two roots. Due to the complexity of the root canal anatomy, root canal treatment were completed with a dental microscope to ensure adequate visualization. After 2 years of regular follow-up examinations, there were no clinical sign or symptom associated with the teeth, and no periapical lesion, was found. This case report describes the characteristic oral features and dental management of TS patients.

KEYWORDS

Turner syndrome, Dental anomalies, Taurodontism

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Journal of the Korean academy of pediatric dentistry 2023 KCI Impact Factor : 0.48

Dental Management in a Patient with Turner Syndrome with Dental Anomalies : A Case Report

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* References for papers published after 2023 are currently being built.

Journal of the Korean academy of pediatric dentistry 2023 KCI Impact Factor : 0.48

Dental Management in a Patient with Turner Syndrome with Dental Anomalies : A Case Report

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KEYWORDS

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