@article{ART001714826},
author={이민정 and KIM JAE GON and Yang Yeon Mi and Byeong Ju Baik and 송희정},
title={DENTAL MANAGEMENT OF PATIENT WITH HUNTER SYNDROME (MUCOPOLYSACCHARIDOSIS TYPE II) : A CASE REPORT},
journal={Journal of the Korean academy of pediatric dentistry},
issn={1226-8496},
year={2012},
volume={39},
number={4},
pages={412-417},
doi={10.5933/JKAPD.2012.39.4.412}
TY - JOUR
AU - 이민정
AU - KIM JAE GON
AU - Yang Yeon Mi
AU - Byeong Ju Baik
AU - 송희정
TI - DENTAL MANAGEMENT OF PATIENT WITH HUNTER SYNDROME (MUCOPOLYSACCHARIDOSIS TYPE II) : A CASE REPORT
JO - Journal of the Korean academy of pediatric dentistry
PY - 2012
VL - 39
IS - 4
PB - The Korean Academy Of Pediatric Dentistry
SP - 412
EP - 417
SN - 1226-8496
AB - Mucopolysaccharidosis (MPS) is a disorder which is caused by the defect of the lysosomal enzyme that is essentially needed for resolution of glycosaminoglycans (GAGs). Metabolite of GAGs will accumulate in the lysosome of cells and will result in the dysfunction of cells, tissues, and organs. Eventually, patients will manifest both mental retardation and physical disorders. In worst cases, mucopolysaccharidosis can cause premature death. The current clinical types have been classified as MPS from type I to type IX according to the defect of certain enzyme. The dental complications have been reported as delay of eruption, enamel hypoplasia, microdontia,malocclusion, condylar defects, gingival hyperplasia and dentigerous cystlike follicle. This clinical report presents the case of a boy with MPS type II, Hunter Syndrome which has various dental complications.
KW - Hunter syndrome;Mucopolysaccharoidosis (MPS) type II;Dental complications;Dental management
DO - 10.5933/JKAPD.2012.39.4.412
ER -
이민정, KIM JAE GON, Yang Yeon Mi, Byeong Ju Baik and 송희정. (2012). DENTAL MANAGEMENT OF PATIENT WITH HUNTER SYNDROME (MUCOPOLYSACCHARIDOSIS TYPE II) : A CASE REPORT. Journal of the Korean academy of pediatric dentistry, 39(4), 412-417.
이민정, KIM JAE GON, Yang Yeon Mi, Byeong Ju Baik and 송희정. 2012, "DENTAL MANAGEMENT OF PATIENT WITH HUNTER SYNDROME (MUCOPOLYSACCHARIDOSIS TYPE II) : A CASE REPORT", Journal of the Korean academy of pediatric dentistry, vol.39, no.4 pp.412-417. Available from: doi:10.5933/JKAPD.2012.39.4.412
이민정, KIM JAE GON, Yang Yeon Mi, Byeong Ju Baik, 송희정 "DENTAL MANAGEMENT OF PATIENT WITH HUNTER SYNDROME (MUCOPOLYSACCHARIDOSIS TYPE II) : A CASE REPORT" Journal of the Korean academy of pediatric dentistry 39.4 pp.412-417 (2012) : 412.
이민정, KIM JAE GON, Yang Yeon Mi, Byeong Ju Baik, 송희정. DENTAL MANAGEMENT OF PATIENT WITH HUNTER SYNDROME (MUCOPOLYSACCHARIDOSIS TYPE II) : A CASE REPORT. 2012; 39(4), 412-417. Available from: doi:10.5933/JKAPD.2012.39.4.412
이민정, KIM JAE GON, Yang Yeon Mi, Byeong Ju Baik and 송희정. "DENTAL MANAGEMENT OF PATIENT WITH HUNTER SYNDROME (MUCOPOLYSACCHARIDOSIS TYPE II) : A CASE REPORT" Journal of the Korean academy of pediatric dentistry 39, no.4 (2012) : 412-417.doi: 10.5933/JKAPD.2012.39.4.412
이민정; KIM JAE GON; Yang Yeon Mi; Byeong Ju Baik; 송희정. DENTAL MANAGEMENT OF PATIENT WITH HUNTER SYNDROME (MUCOPOLYSACCHARIDOSIS TYPE II) : A CASE REPORT. Journal of the Korean academy of pediatric dentistry, 39(4), 412-417. doi: 10.5933/JKAPD.2012.39.4.412
이민정; KIM JAE GON; Yang Yeon Mi; Byeong Ju Baik; 송희정. DENTAL MANAGEMENT OF PATIENT WITH HUNTER SYNDROME (MUCOPOLYSACCHARIDOSIS TYPE II) : A CASE REPORT. Journal of the Korean academy of pediatric dentistry. 2012; 39(4) 412-417. doi: 10.5933/JKAPD.2012.39.4.412
이민정, KIM JAE GON, Yang Yeon Mi, Byeong Ju Baik, 송희정. DENTAL MANAGEMENT OF PATIENT WITH HUNTER SYNDROME (MUCOPOLYSACCHARIDOSIS TYPE II) : A CASE REPORT. 2012; 39(4), 412-417. Available from: doi:10.5933/JKAPD.2012.39.4.412
이민정, KIM JAE GON, Yang Yeon Mi, Byeong Ju Baik and 송희정. "DENTAL MANAGEMENT OF PATIENT WITH HUNTER SYNDROME (MUCOPOLYSACCHARIDOSIS TYPE II) : A CASE REPORT" Journal of the Korean academy of pediatric dentistry 39, no.4 (2012) : 412-417.doi: 10.5933/JKAPD.2012.39.4.412