Dental Management in a Patient with Congenital Insensitivity to Pain with Anhidrosis : A Case Report

Cheolhyeon Bae (배철현); LEE DAE-WOO (이대우); KIM JAE GON (김재곤); Yang Yeon Mi (양연미)

doi:10.5933/JKAPD.2019.46.4.416

Dental Management in a Patient with Congenital Insensitivity to Pain with Anhidrosis : A Case Report

Journal of the Korean academy of pediatric dentistry
Abbr : J Korean Acad Pediatr Dent
2019, 46(4), pp.416-421
DOI : 10.5933/JKAPD.2019.46.4.416
Publisher : The Korean Academy Of Pediatric Dentistry
Research Area : Medicine and Pharmacy > Dentistry
Received : June 20, 2019
Accepted : August 5, 2019
Published : November 27, 2019

Cheolhyeon Bae ¹, LEE DAE-WOO ¹, KIM JAE GON ¹, Yang Yeon Mi ¹

¹전북대학교

Accredited

ABSTRACT

Congenital insensitivity to pain with anhidrosis (CIPA) is a rare, autosomal recessive disorder; affected patients are characterized by inability to feel pain and to sweat over the entire body, as well as by mental retardation. Because, in the oral examination, no specific findings on soft or hard tissue may be found except possible lesions due to selfmutilation, early recognition and diagnosis are essential for these patients. Pediatric dentists must be aware of the clinical manifestations and treatment considerations related to uncontrolled body temperature, tactile hyperesthesia and lack of pain reflex. In this case report, dental management of CIPA was suggested by presenting a 6-year follow-up of young patient.

KEYWORDS

CIPA, Pain insensitivity, Anhidrosis, Self-mutilation

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* References for papers published after 2023 are currently being built.

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Journal of the Korean academy of pediatric dentistry 2023 KCI Impact Factor : 0.48

Dental Management in a Patient with Congenital Insensitivity to Pain with Anhidrosis : A Case Report

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* References for papers published after 2023 are currently being built.

Journal of the Korean academy of pediatric dentistry 2023 KCI Impact Factor : 0.48

Dental Management in a Patient with Congenital Insensitivity to Pain with Anhidrosis : A Case Report

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